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DeCS
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Descriptor English:
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Jaundice, Chronic Idiopathic
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Descriptor Spanish:
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Ictericia Idiopática Crónica
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Descriptor Portuguese:
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Icterícia Idiopática Crônica
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Synonyms English:
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Dubin-Johnson Syndrome
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Tree Number:
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C16.320.565.300.764
C16.614.451.500.250
C18.452.648.300.764
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Definition English:
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A benign, autosomally recessive inherited hyperbilirubinemia characterized by the presence of a dark pigment in the centrilobular region of the liver cells. There is a functional defect in biliary excretion of bilirubin, cholephilic dyes, and porphyrins. Affected persons may be asymptomatic or have vague constitutional or gastrointestinal symptoms. The liver may be slightly enlarged, and oral and intravenous cholangiography fails to visualize the biliary tract. |
Allowable Qualifiers English:
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Record Number:
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7735
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Unique Identifier:
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D007566
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Occurrence in VHL:
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Similar:
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DeCS CID-10 SciELO LILACS LIS
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